İstanbul Üniversitesi İstanbul Tıp Fakültesi Çocuk Sağlığı ve Hastalıkları AD, İstanbul, Türkiye

Aim: We aimed to determine the morphological and clinical features of non-valvular aortic stenosis cases, who have attended our Pediatric Cardiology Clinic for thelast three years. Material and Method: Thirty-two children with non-valvular aortic stenosis, who attended our clinic between January 2003 and 2006, were retrospectively evaluated. Transthoracic echocardiography was conducted to all cases and the underlying pathology which resulted in stenosis, the degree, the additional abnormalities, the surgical necessities and the results were taken into evaluation. Results: Twenty in 32 cases had subvalvular aortic stenosis. They were 13 boys and seven girls and their mean age was 11.2 ± 3.6 years, their mean age at the time of diagnosis was 6.2 ± 3.6 years. The peak systolic gradient, measured from the left ventricle outflow tract was 43.9 ± 27.6 mmHg. Twelve cases had supravalvular aortic stenosis and six of them were boys. Their mean age, their age at the time of diagnosis and peak systolic pressure gradient on echocardiography were 7.1 ± 5.3, 4.1 ± 4.0 years and 42.4 ± 8.9 mmHg, respectively. Seven Williams syndrome cases were diagnosed among these patients. Conclusions: The patients with non-valvular aortic stenosis should be carefully evaluated for their specific morphological and clinical differences and followed-up closely.